Abstract
Retroperitoneal paragangliomas are rare tumors.They usually present abdominal pain and mass clinically. A literature review suggests that only a few cases have been reported so far. A case of giant retroperitoneal paraganglioma 20x30 cm in size with extraadrenal origin in a 66-year-old patient is reported alongside with its clinical presentation, diagnosis, surgical management and literature review.
Keywords:
Extraadrenal paraganglioma, retroperitoneal tumor
References
1
Rha SE, Byun JY, Jung SE, Chun HJ, Lee HG, Lee JM. Neurogenic tumors in the abdomen: tumor types and imaging characteristics. Radiographics 2003;23:29-43.
2
Lack EE, Cubilla AL, Woodruff JM, Lieberman PA. Extraadrenal paraganglioma of the retroperitoneum. Am J Surg Pathol 1980;4:109-120.
3
Ahmad S, Cathy D, Sheikh M, Sweeney P. Retroperitoneal extra-adrenal paraganglioma: a rare but important diagnosis. Ir J Med Sci 2009;178:211-214.
4
Absher KJ, Witte DA, Truong LD, Ramzy I, Mody DR, Ostrowski ML. Aspiration biopsy of osseous metastasis of retroperitoneal paraganglioma. Report of a case with cytologic features and differential diagnostic considerations. Acta Cytol 2001;45:249-253.
5
Lack EE, Cubila AL, Woodruf JM, Farr HW. Paragangliomas of the head and neck region: A clinical study of 69 patients. Cancer 1977; 39:397-409.
6
Linnoila RI, Keiser HR, Steinberg SM, Lack EE. Histopathology of benign versus malignant sympathoadrenal paragangliomas: Clinicopathologic study of 120 cases including unusual histologic features. Hum Pathol 1990;21:1168-1180.
7
O'Riordain DS, Young WF, Grant CS, Carney JA, Van Heerden JA: Clinical spectrum and outcome of functional extraadrenal paraganglioma. World J Surg 1996;20:916-922.
8
Matsui H, Ikeuchi S, Onoda N, Tsutsumi Y. Malignant paraganglioma of the retroperitoneum with lung metastases: A 13- year survior after radical surgery. Asian J Surg 2007; 30:75-79.
9
Oguma S, Okazaki H, Nakamichi G, Endo Y. A case of nonfunctioning paraganglioma arising from the retroperitoneum: angiographic features. J Urol 1985;133:73-76.
10
Massey V, Wallner K. Treatment of metastatic chemodectoma. Cancer 1992;69: 790-792.
11
Sclafani LM, Woodruff JM, Brennan MF: Extraadrenal retroperitoneal paragangliomas: Natural history and response to treatment. Surgery 1990, 108:1124-1130.
12
Patel SR, Winchester DJ, Benjamin RS. A 15-year experience with chemotherapy of patiens with paraganglioma. Cancer 1995;76:1476-1480.
13
He J, Makey D, Fojo T et al. Successful chemotherapy of hepatic metastases in a case of succinate dehydrogenase subunit B-related paraganglioma. Endocrine 2009;36:189-193.
14
Hruby G, Lehman M, Barton M, PedutoT. Malignant retroperitoneal paraganglioma: Case report and review of treatment options. Australas Radiol 2000;44:478-482.
15
Buonuomo V, Ruggiero A, Rando G et al. Malignant retroperitoneal paraganglioma: case report and review of the literature. Pediatr Hematol Oncol 2004;21:731- 738.
